Rare Dementias

A detailed consideration of the neurodegenerative diseases that can cause parkinsonism including dementia with Lewy bodies (DLB), multiple system atrophy (MSA), progressive supranuclear palsy (PSP) and corticobasal degeneration (CBD).

Diagnosis, pharmacologic management, non-pharmacologic management, and other considerations. This material is provided by UCSF Weill Institute for Neurosciences as an educational resource for health care providers.

a systematic review of studies reporting incidence and prevalence of CBS and PSP. While some epidemiological studies have used the term corticobasal degeneration (CBD) we have used the term CBS throughout, as denoting the clinical syndrome. We have reserved the term CBD for the pathological diagnosis.
Lyons, S., Trépel, D., Lynch, T., Walsh, R., & O'Dowd, S. (2023). The prevalence and incidence of progressive supranuclear palsy and corticobasal syndrome: a systematic review and meta-analysis. Journal of neurology, 270(9), 4451–4465.

CurePSP is the leading nonprofit organization dedicated to the awareness, care and cure for three neurodegenerative diseases: progressive supranuclear palsy (PSP), corticobasal degeneration (CBD) and multiple system atrophy (MSA). As a catalyst for new treatments and a cure, we establish important partnerships and fund critical research. Through our advocacy and support efforts, we enhance education, care delivery and quality of life for people living with PSP, CBD and MSA and their families. Science, community and hope are at the heart of CurePSP’s mission and all of our services.